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KMID : 1035620220100020080
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Allergy Asthma & Respiratory Disease
2022 Volume.10 No. 2 p.80 ~ p.88
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Diagnosis and treatment of hereditary angioedema: An expert opinion
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Jung Jae-Woo
Park So-Young
Yoon Sun-Young
Kim Gun-Woo
Sohn Kyoung-Hee
Kang Sung-Yoon
Park Hye-Jung
Kang Min-Kyu
Kim Joo-Hee
Park Kyung-Hee
Suh Dong-In
Lee Dong-Hun
Kim Sae-Hoon
Kwon Hyouk-Soo
Kang Hye-Ryun
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Abstract
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Hereditary angioedema (HAE) is a rare disease, but it severely interrupts daily life activities and can sometimes be life-threatening. Therefore, early diagnosis and prompt treatment of HAE attacks are critical. Physicians should be aware of how to diagnose and manage HAE to prepare not to miss a diagnosis when treating HAE patients. Physicians must also carry out tests to confirm the diagnosis of HAEs caused by C1 inhibitor deficiency (type 1) or C1 inhibitor dysfunction (type 2) in patients with recurrent angioedema. In addition, recent studies revealed another type of HAE which is not related to C1 inhibitor (normal C1 inhibitor HAE). Once HAE is confirmed, patients and their caregivers should be given with short-term and long-term treatment plans to relieve or prevent HAE attacks. HAE requires life-long measures, including psychological support for patients and self-management education.
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KEYWORD
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Hereditary angioedema, Bradykinin, C1-inhibitor, Diagnosis, Management
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